Pulmonary artery agenesis.

Pulmonary artery agenesis is one of several diagnostic possibilities which may present with similar chest roentgenographic features, including unilateral pulmonary hypoperfusion and nonvisualization of a pulmonary artery. We have applied ventilation and perfusion scintiphotography as an aid in differentiating agenesis from the other conditions with which it may be confused. Four patients presenting with the chest roentgenographic features suggestive of pulmonary artery agenesis were evaluated, when possible, with complete pulmonary function studies, bronchography, cardiac catheterization, and pulmonary and aortic angiography. In all patients, the distribution of ventilation and perfusion